Piebaldism: rare but all dermatologists have heard this strange term during residency
- This term comes from the Greek word:
- συριγξ = surinx = canal. The word is pronounced as ” surinx”.
- This origin is used in other medical fields (syringomyelia, syringobulbia, syringotomy)
- Information on Syringoma:
- Syringoma develop from the excretory lining of eccrine glands
- They are frequent benign tumors and affect more often females with familial forms. Other individuals more at risk are those with Down syndrome.
- They present clinically as firm skin-colored or slightly pigmented papules.
- They are located preferably on the inferior eyelids, but can extend to the neck and the anterior thorax.
- Widespread forms have also been described with involvement of the external genitalia.
- Treatment is not always satisfactory. Scars can result either from the treatment of the small lesions with electrocauthery (high-wave), or from the excision of the bigger ones.
- Note: depending on the part of the eccrine gland which is involved, histopathologists distinguish several tumors such as hidrocystoma, hidradenoma, spiradenoma, cylindroma, poroma and so on.
Contributors
Dr Christophe Hsu – dermatologist. Geneva, Switzerland
Source of information:
-Harms M. Dermatologica Helvetica (The Swiss Journal of Dermatology and Venereology: www.dermatologicahelvetica.com
Related posts